hypoplastic left heart syndrome


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hypoplastic left heart syndrome

 
congenital hypoplasia or atresia of the left ventricle, the aortic or mitral valve, and the ascending aorta, with respiratory distress, cardiac failure, and death in infancy.

hy·po·plas·tic left heart syn·drome

[MIM*241550]
association of underdevelopment of the left heart chambers with atresia or stenosis of the aortic and/or mitral valve and hypoplasia of the ascending aorta.

hypoplastic left heart syndrome

Pediatric cardiology A group of congenital often AR cardiac defects characterized by hypo- or agenesis of the left ventricle, aortic and mitral valves, an atrial right-to-left shunt; right-sided hypoplasia of tricuspid or pulmonary valves, pulmonary stenosis, or right ventricular hypoplasia; the ascending and transverse aorta is narrowed with a diaphragm-like aortic coarctation at the preductal aortic isthmus; postnatal life hinges on adequate blood supply–ie, is ductus dependent, unrestricted atrial shunting, and a balance between the pulmonary and systemic vascular resistances; surgery is difficult as there are extensive malformations Mortality High. See Baby Fae heart.
References in periodicals archive ?
The study also is enrolling control patients who do not receive cell delivery because hypoplastic left heart syndrome was not diagnosed before birth or cord blood was not collected.
Over 900 cardiac operations are performed annually (http://heart.chop.edu/hrtdisors.html) * Forthcoming Text: Hypoplastic Left Heart Syndrome, edited by H.A.
OKLAHOMA CITY OU Medicine has earned membership in the national Hypoplastic Left Heart Syndrome Consortium for its surgeons' expertise in treating babies born with HLHS.
Hypoplastic left heart syndrome is a rare and often fatal heart condition caused by an underdeveloped heart.
He was in desperate need of a transplant after being born on October 2 with hypoplastic left heart syndrome condition - which means the left side of the organ is underdeveloped and cannot work properly.
They said Charlie, who had hypoplastic left heart syndrome, had responded well.
Louis was born with Hypoplastic Left Heart Syndrome, meaning the left part of the heart is very small and doesn't work.
The single mum-of-four, who has one-year-old Freddie, three-year-old Alexis and seven-year-old Jack was told at her 20-week scan that Jacob had hypoplastic left heart syndrome, which means the left hand side of his heart did not form properly.
Saifuddin Ahmed Helal was born on May 12 with a rare condition known as hypoplastic left heart syndrome in which part of the heart that pumps oxygenated blood to the rest of the body is underdeveloped.
Tom was born with hypoplastic left heart syndrome, which means the left side of his heart is underdeveloped.
Scarlett, of Pallister Park, was born on July 13 with the rare condition hypoplastic left heart syndrome with an intact atrial septum - a rare combination which meant only half her heart was operating.
The charity is the one chosen by George, who suffers from a rare congenital condition known as hypoplastic left heart syndrome (HLHS), in which the left ventricle of the heart is almost non existent.