There was no problem/ controversy regarding diagnosis of aganglionosis but when we talk of ganglionic segments actually it may include the normal number of ganglion cells and allied HDs, which are hypoganglionosis
, hyperganglionosis and immature ganglion cells.
Malformations in the reserved segment are mainly type B intestinal neuronal dysplasia and hypoganglionosis.
Patterns of postoperative enterocolitis in children with Hirschsprung's disease combined with hypoganglionosis.
Total colonic aganglionosis is often associated with a long transition zone characterized by hypoganglionosis
and the presence of abnormal immature cells individually and in clusters.
2-4) This paper reports a patient with a history of cerebrovascular accident presenting with sigmoid volvulus secondary to megacolon with hypoganglionosis.
Although the overwhelming likely hood is that the marked hypoganglionosis was a consequence of the central nervous system disease, other possible etiologies needed to be considered.
Megacolon in an adult case of hypoganglionosis, a pseudo-Hirschsprung's disease: an autopsy study.
Other neuronal abnormali ties included isolated hypoganglionosis, immaturity of ganglion cells and isolated hyperganglio nosis (IND Type B).
Key words: Hirschsprung's disease (HD), hypoganglionosis, hyperganglionosis (IND type B) and immaturity of ganglion cells (IGC).
Congenital intestinal neuronal disturbances have been classified as aganglionosis (Hirschsprung's di sease), hyperganglionosis (Intestinal Neuronal Dys plasia), hypoganglionosis, ganglion cell immaturity, combined forms and certain unclassifiable forms.
8 Almost all cases reported in literature occurred relatively late in chil dhood9 and the common complaint of the patients with hypoganglionosis is intractable constipation.