hydranencephaly


Also found in: Encyclopedia, Wikipedia.

hydranencephaly

 [hi″dran-en-sef´ah-le]
absence of the cerebral hemispheres, their normal site being occupied by cerebrospinal fluid.

hy·dran·en·ceph·a·ly

(hī'dran-en-sef'ă-lē),
Absence of cereberal hemispheres, which have been replaced by fluid-filled sacs, lined by leptomeninges. The cranium and its brain cavities, however, are normal.
[hydr- + G. an- priv. + enkephalos, brain]

hy·dran·en·ceph·a·ly

(hī'dran-en-sef'ă-lē)
Complete or nearly complete absence of cerebral hemispheres, which have been replaced by fluid-filled sacs lined by leptomeninges. The cranium and its fossae are normal.
[hydr- + G. an- priv. + enkephalos, brain]
References in periodicals archive ?
(1985) Hydranencephaly: US appearance during in utero evolution.
Zika Virus Infection and Stillbirths: A Case of Hydrops Fetalis, Hydranencephaly and Fetal Demise.
The toddler, who is being treated at the Philippines Children's Medical Center in Pasig, a city in the metropolitan district of Manila, is fighting to survive hydranencephaly that doesn't allow the brain to develop and can cause disability, intellectual problems, seizures and vision problems. The condition is incurable and treatment involves using a tube to drain fluid out of the skull.
Zika/associated birth defects include selected congenital brain anomalies (intracranial calcifications; cerebral atrophy; abnormal cortical formation; corpus callosum abnormalities; cerebellar abnormalities; porencephaly; hydranencephaly; ventriculomegaly/hydrocephaly); selected congenital eye anomalies (microphthalmia or anophthalmia; coloboma; cataract; intraocular calcifications; chorioretinal anomalies involving the macula, excluding retinopathy of prematurity; and optic nerve atrophy, pallor, and other optic nerve abnormalities); and/or microcephaly at birth (birth head circumference <3rd percentile for infant sex and gestational age based on INTERGROWTH/21st online percentile calculator [http://intergrowth21.ndog.ox.ac.uk/]).
CPC may also be an option for cases with high chance of shunt complication such as hydranencephaly and as an adjunct therapeutic measure for complex cases of hydrocephalus such as multiloculated hydro cephalus.
This association was demonstrated in a report from Salvador, Brazil, which showed a fetus miscarriage (32nd week) with microcephaly, hydranencephaly, intracranial calcifications and destructive lesions of posterior fossa.
The study showed the baby's brain was absent, a condition known as hydranencephaly. Instead of tissue, the brain cavities were filled with fluid.
Two cases of hemifacial microsomia where there was evidence of carotid artery occlusion (28) and a case where the subject lacked an internal carotid artery and showed subsequent facial defects and unilateral hydranencephaly (29) have been reported.
Results Out of 11,500 pregnant women, CNS anomalies were detected in 48 cases.They included hydrocephalus in 21(43.8%) anencephaly in 11(22.9%), spina bifida in 8(16%), 02 each (4.1%) with encephalocele, arachnoid cysts, hydranencephaly and 01 each with exencephaly and holoprosencephaly.
Morphogenesis of hydranencephaly and other intracranial malformations in progeny of pregnant ewes infected with pestiviruses.
(1) Cerebral damage can be severe, as cases of hydranencephaly with arterial and venous malformations have been reported.