persistent mullerian duct syndrome

(redirected from hernia uteri inguinale)

per·sis·tent mül·le·ri·an duct syn·drome

familial disorder with presence of fallopian tube, uterus, and testis in a male. Deficient müllerian inhibitory substance secondary to Sertoli cell defect.

persistent müllerian duct syndrome

A rare form of male pseudohermaphroditism of childhood onset, which is characterised by persistence of müllerian duct (“female”) structures in a phenotypically normal male.
 
Clinical findings
Cryptorchidism, testicular hypoplasia, normal virilisation at puberty, increased testicular tumours and transverse testicular ectopia.
References in periodicals archive ?
Although hernia uteri inguinale is a very rare disorder in phenotypic male, a preoperative diagnosis would be helpful in surgical planning.