hemoglobin Bart

he·mo·glo·bin Bart

[MIM*142309]
a Hb homotetramer (all four polypeptides identical) of formula γ4, found in the early embryo and in α-thalassemia 2; not effective in oxygen transport; does not display a Bohr effect.

hemo·glo·bin Bart

(hē'mō-glō'bin bahrt)
An Hb homotetramer (all four polypeptides identical) of formula γ4, found in the early embryo and in α-thalassemia 2; not effective in oxygen transport; does not display a Bohr effect.
Synonym(s): haemoglobin Bart.
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References in periodicals archive ?
It is present in two clinically significant forms: hemoglobin Bart hydrops fetalis (Hb Bart) syndrome and hemoglobin H (HbH) disease.
Hemoglobin Bart hydrops (Hb Bart syndrome) and hemoglobin H (HbH) disease are the two most significant forms of a-thalassemia seen in clinics.
Alpha thalassemia deletions found in suspected cases of beta thalassemia major in Pakistani population
Sonographic markers of hemoglobin Bart disease at midpregnancy.
A multiplex quantitative fluorescent PCR test for prenatal diagnosis of Hb baits hydrops fetalis

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