From the Archives of the AFIP: pulmonary veno-occlusive disease and pulmonary capillary hemangiomatosis
Hemangiomatosis refers to a rare condition in which the liver parenchyma is replaced by hemangiomatous lesions with ill-defined borders.
Association of hepatic hemangiomatosis with giant cavernous hemangioma in the adult population: Prevalence, imaging appearance, and relevance.
Hurvitz SA, Hurvitz CH, Sloninsky L, Sanford MC: Successful treatment with cyclophosphamide of life-threatening diffuse hemangiomatosis
involving the liver.
In contrast, PVNS, synovial hemangiomatosis, and lipoma are usually located in the infrapatellar fat pad of Hoffa.
In conclusion, in children or adolescent patients with mono/oligoarticular effusion and synovial hypertrophy without systemic involvement, synovial chondromatosis, PVNS, synovial hemangiomatosis, and LA should be considered in the differential diagnosis.
associated with brachial plexus palsy.
4 Associated with significant venous or capillary involvement Pulmonary veno-occlusive disease (PVO) Pulmonary capillary hemangiomatosis
Other benign vascular proliferations include epithelioid or histiocytoid hemangioendothelioma and diffuse sinusoidal hemangiomatosis
DIAGNOSIS: Splenic hemangiomatosis with incidental clear cell renal carcinoma.
This finding confirmed the diagnosis of splenic hemangiomatosis as opposed to lymphangiomatosis or peliosis.
Idiopathic pulmonary arterial hypertension (PAH) is included in Group 1 of PAH classification, while pulmonary veno- occlusive disease (PVOD), pulmonary capillary hemangiomatosis
(PCH), portopulmonary hypertension (PoPH) and HIV-associated PAH constitute the subgroups of Group I PAH disorders.