glycogenosis type 6
gly·co·ge·no·sis type 6
glycogenosis due to hepatic glycogen phosphorylase deficiency, resulting in accumulation of glycogen of normal chemical structure in liver and leukocytes.
Synonym(s): hepatophosphorylase deficiency glycogenosis, Hers disease
Farlex Partner Medical Dictionary © Farlex 2012
gly·co·ge·no·sis type 6
(glī'kō-jĕ-nō'sis tīp)Disorder due to hepatic glycogen phosphorylase deficiency, resulting in accumulation of glycogen of normal chemical structure in liver tissue and leukocytes.
Synonym(s): Hers disease.
Synonym(s): Hers disease.
Medical Dictionary for the Health Professions and Nursing © Farlex 2012