giant-cell fibroblastomaA rare solitary mesenchymal tumour, classified by the WHO as a fibrohistiocytic tumour of intermediate malignancy, which is related to dermatofibrosarcoma protuberans.
Occurs in children, usually under age 5, often in the superficial soft tissues of the thigh, back, sacrum and inguinal region.
Best option for cure is careful resection of margins with Moh’s surgery.
Locally aggressive, up to 50% recurrence; does not metastasise.
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