In 20% of patients, the BVP is associated with gangliopathy
, described in 2011 as CANVAS (cerebellar ataxia, nonlength-dependent sensory neuropathy, vestibular areflexia) , while 50% of the idiopathic BVH patients present with migraine according the International Headache Society criteria .
An electromyography revealed sensorial gangliopathy
. On physical examination the positioning and the vibration sensations of the patient were found to be diminished.
This infection gives rise to vesiculation and ulceration of the external ear and ipsilateral anterior two thirds of the tongue and soft palate, as well as ipsilateral facial neuropathy (in Cranial Nerve VII), radiculoneuropathy or geniculate gangliopathy
. VZV infection or reactivation involving the geniculate ganglion of CN VII within the temporal bone is the main pathophysiological mechanism of Ramsay Hunt Syndrome.