Specifically, histologically, there was no granulomatous disease or lymphocytic interstitial pneumonia pattern present suggestive of granulomatous-lymphocytic interstitial lung disease (GLILD) and there was no interstitial elastosis suggestive of pleuroparenchymal fibroelastosis
A new presentation of neonatal Lupus: 5 cases of isolated mild endocardial fibroelastosis
associated with maternal Anti-SS/Ro and Anti-SSB/La antibodies.
6 In a series of 72 children under 12 years with echo diagnosis of cardiomyopathy over a two-year period at the National Institute of Cardiovascular Diseases, Karachi, HCM was reported in 31 (43 Percent), endocardial fibroelastosis
in 18 (25 Percent), RCM in 10 (14 Percent) and DCM in 7 (10 Percent) cases.
told the story of her rare heart disease called endocardial fibroelastosis
, an inherited disorder in which synthesis of carnitine is disturbed.
sup] Due to the lack of specificity in its clinical manifestations, ALCAPA might be misdiagnosed as dilated cardiomyopathy, endocardial fibroelastosis
, or mitral valve lesions.
In 1992, the entity of idiopathic pulmonary upper lobe fibrosis was described by Amitani et al (1) in Japan, and this disease shows a predilection for upper lobe involvement where pleural fibrosis and adjacent lung parenchymal fibroelastosis
Lymphstasis in cardiac lymphatics has been associated with decreased cardiac output, conductive disturbances, arrhythmias, bacterial endocarditis, rheumatic valvulitis and endocardial fibroelastosis
, infiltrative cardiomyopathy, eosinophilic endomyocardial disease, cords, and false tendons are often present in normal hearts, and should also be considered (8).
Intimal thickening and fibroelastosis
of the vascular wall are frequent histological findings in Moyamoya disease (9).
Of course, there are many other causes of pulmonary fibrosis to consider, including smoking-related disease, pneumoconiosis, sarcoidosis/berylliosis, immunoglobulin G4-related disease, ErdheimChester disease (Figure 3, D), Hermansky-Pudlak syndrome, and idiopathic pleuroparenchymal fibroelastosis
Among these 37 patients, 11 had an isolated CoA, including four patients diagnosed with dilated cardiomyopathy, endocardial fibroelastosis
and left ventricular noncompaction, before being referred to our hospital.