Rare cases might show a few intracytoplasmic vacuoles characteristic of epithelioid hemangioendothelioma
Keratins MNF116 and CAM5.2, epithelial membrane antigen (EMA), CD31, and CD34 were also negative, as was CAMTA1, a recently described antibody expressed in epithelioid hemangioendothelioma
(Table 1 and Fig.
(EHE) is a rare endothelial neoplasm first described by Weiss and Enzinger (1) in 1982.
One case was that of epithelioid hemangioendothelioma
Approximately 10% of cases are associated with other developmental anomalies or syndromes, including early-onset varicose veins, lymphedema, Klippel-Trenaunay-Weber syndrome, Maffucci syndrome, epithelioid hemangioendothelioma
, and superficial cutaneous lymphatic malformations .
(EHE) is a rare vascular neoplasm that occurs more often in women than men and usually arises within the liver, but can also present within other tissues including lung, bone, or peritoneum .
Pulmonary epithelioid hemangioendothelioma
(PEH) is a rare neoplasm of vascular origin.
Levasseur, "Epithelioid hemangioendothelioma
of the azygos vein," Archives des Maladies du coeur et des Vaisseaux, vol.
of the spleen is very similar to its liver counterpart (i.e.
Unlike cutaneous epithelioid angiomatous nodule, the lesions were not composed of solid sheets of epithelioid endothelial cells.16 The absence of bacilli, acute neutrophilic inflammation, and capillary proliferation typical of pyogenic granuloma ruled out bacillary angiomatosis.16 Distinction from epithelioid hemangioendothelioma
was made by the lesion's architecture and the presence of prominent inflammation and numerous well-formed blood vessels, with a lack of extravascular proliferation of epithelioid neoplastic cells.16
(EHE) is a rare vascular tumor with an estimated prevalence of less than one in one million.
Epithelioid hemangioma is a benign lesion and must be distinguished by the pathologist from epithelioid hemangioendothelioma
and epithelioid angiosarcoma, which are low- and high-grade malignancies, respectively.[sup.7]