Clinically, RE presents as epilepsia partialis continua
(EPC) followed by hemiparesis and cognitive impairment, which gradually progresses with the disease activity.
These tests are particularly important if the myoclonus is limited to a particular area of the body or if the child is suspected of having a rare form of epilepsy known as epilepsia partialis continua. Since certain viral infections may cause myoclonus, a spinal tap is sometimes necessary in order to test for such infections.
* Epileptic myoclonus including juvenile myoclonic epilepsy, progressive myoclonic epilepsies (PME), epilepsia partialis continua, Rasmussen's encephalitis, early infantile myoclonic encephalopathy, infantile spasms (also known as West syndrome), Lennox-Gastaut syndrome, benign familial myoclonic epilepsy, and Angelman syndrome; and
Localization-related epilepsies: Simple partial seizures, complex partial seizures, benign focal epilepsy of childhood, and epilepsia partialis continua
. In W.E.
Epilepsia partialis continua
consists of repetitive focal muscle contractions of the fingers and corner of the mouth, persisting for days or weeks without loss of consciousness and is often refractory to medical therapy.
In this case, focal seizures occur if the cerebral cortex is affected primarily (focal motor seizures including most frequently epilepsia partialis continua
) and dyskinesias occur, if the subcortical structures are affected primarily (4,8,9).
INTRODUCTION: "Epilepsia Partialis Continua" is considered as the status epilepticus equivalent of simple partial motor seizures.
DISCUSSION: The estimated the prevalence of epilepsia partialis continua at less than 1 case per million population [Cockerell et al (1996)].
PATHOLOGY: The term "epilepsia partialis continua" is restricted to jerks of cortical origin.
PROGNOSIS: The prognosis of epilepsia partialis continua is dictated by its underlying etiology.
CONCLUSION: Epilepsia Partialis Continua is a rare form of seizure disorder which involves focal muscle twitching for prolonged periods of time.
Clinical and physiological features of epilepsia partialis continua. Cases ascertained in the UK.