malignant endovascular papillary angioendothelioma

(redirected from endovascular papillary angioendothelioma)

malignant endovascular papillary angioendothelioma

A rare, low-grade malignant vascular tumour of infants and children, which involves the spleen and is characterised by cavernous lymphangioma-like features.
 
Prognosis
Death is rare.
References in periodicals archive ?
Malignant endovascular papillary angioendothelioma of the skin in childhood: clinicopathologic study of 6 cases.
Clinically, IPEH can be misdiagnosed as a mucocele, hemangioma, pyogenic granuloma, Kaposi sarcoma, angiosarcoma, Kimura disease, intravenous atypical vascular proliferation, endovascular papillary angioendothelioma, papular angioplasia, or bacillary angiomatosis.
Endovascular papillary angioendotheliomas are histologically similar to IPEH, but they can be differentiated by their more columnar endothelial cells and their lymphatic component.