malignant endovascular papillary angioendothelioma

(redirected from endovascular papillary angioendothelioma)

malignant endovascular papillary angioendothelioma

A rare, low-grade malignant vascular tumour of infants and children, which involves the spleen and is characterised by cavernous lymphangioma-like features.
 
Prognosis
Death is rare.
References in periodicals archive ?
Malignant endovascular papillary angioendothelioma of the skin in childhood: clinicopathologic study of 6 cases.
Clinically, IPEH can be misdiagnosed as a mucocele, hemangioma, pyogenic granuloma, Kaposi sarcoma, angiosarcoma, Kimura disease, intravenous atypical vascular proliferation, endovascular papillary angioendothelioma, papular angioplasia, or bacillary angiomatosis.
Endovascular papillary angioendothelioma of childhood: A vascular lesion possibly characterized by "high" endothelial cell differentiation.