embryonal sarcoma

embryonal sarcoma

A nonspecific term for a primitive malignant mesenchymal tumour, which requires qualifiers to inform the nature of the cancer, such as:
(1) Undifferentiated embryonal sarcoma of the liver;
(2) Embryonal rhabdomyosarcoma;
(3) Nephroblastoma/Wilms tumour.
References in periodicals archive ?
Over the next few days, tests gave a more specific diagnosis: Undifferentiated Embryonal Sarcoma of the Liver (UESL), a diagnosis so rare her doctor said he had only come across four cases in 20 years.
Undifferentiated embryonal sarcoma of the liver (UESL), first described by Stocker and Ishak in 1978 as a rare aggressive mesenchymal tumor of the liver [2], accounts for approximately 9-13% of all childhood malignant hepatic tumors [3] and is the third most common hepatic malignancy in children after hepatoblastoma and hepatocellular carcinoma.
Malignant MEST with a sarcomatous stromal component shows morphologic overlap with primary renal synovial sarcoma (RSS) (formerly "embryonal sarcoma of the kidney") [33].
Undifferentiated embryonal sarcoma of the liver (UESL) is an extremely rare neoplasm in adults with less than 60 cases described so far in the literature [1-7].
BENIGN MALIGNANT EPITHELIAL Focal nodular Hepatoblastoma hypoplasia Hepatocellular Hepatocellular carcinoma adenoma Nodular Fibrolamellar regenerative carcinoma hyperplasia Mixed hamartoma Developmental cysts MESENCHYMAL Infantile Undifferentiated/ hemangioendothelioma embryonal sarcoma Mesenchymal Angiosarcoma hamartoma Cavernous Rhabdomyosarcoma hemangioma Infantile Rhabdoid tumor pseudotumor GERM CELL TUMORS TERATOMA Endodermal sinus tumor Benign liver tumors are rare and often present in infancy.
Management of undifferentiated embryonal sarcoma of the liver in children: A case series and management review.
At just 14 the teenager was believed to be only the second person in the country to be diagnosed with undifferentiated embryonal sarcoma of the liver.
Other malignant tumours were undifferentiated embryonal sarcoma and biliary rhabdomyosarcoma.
Her cancer is called undifferentiated hepatic embryonal sarcoma, a difficult-to-treat liver cancer that is complicated in Ashley's case by the fact that the tumor has impinged upon the blood vessels supplying her liver.
McCarville et al (44) evaluated PET-CT scanning of childhood sarcomas including rhabdomyosarcoma, Ewing sarcoma, nonrhabdomyosarcoma soft-tissue sarcoma, osteosarcoma, chondrosarcoma and embryonal sarcoma. The researchers concluded that PET-CT is useful in depicting an unknown primary rhabdomyosarcoma and detecting unsuspected and unusual metastatic sites of childhood sarcomas.
The term undifferentiated embryonal sarcoma of the liver (UESL) was introduced by Stocker and Ishak (1) in 1978 to describe groups of mesenchymal tumor in the liver that did not show evidence of differentiation.