ectopia lentis


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Related to ectopia lentis: Ectopia Lentis et Pupillae

ectopia

 [ek-to´pe-ah] (L.)
malposition, especially if congenital.
ectopia cor´dis congenital displacement of the heart outside the thoracic cavity.
ectopia len´tis displacement of the crystalline lens of the eye.

ec·to·pi·a len·'tis

[MIM*225100]
displacement of the lens of the eye.
Synonym(s): dislocation of lens

ec·to·pi·a len·tis

(ek-tō'pē-ă len'tis)
Displacement of the lens of the eye.

Ectopia lentis

Dislocation of the lens of the eye. It is one of the most important single indicators in diagnosing Marfan syndrome.
Mentioned in: Marfan Syndrome

luxation of the lens

Pathological and complete dislocation of the lens relative to the pupil. If the luxation is incomplete it is called subluxation of the lens (or dislocation or ectopia lentis). Subluxation is one of the causes of monocular diplopia. If the luxation is complete the eye becomes markedly hyperopic and is unable to accommodate. Luxation occurs in contusion of the globe, in many ocular (e.g. buphthalmos) and other diseases (e.g. syphilis) or it can be inherited (e.g. the bilateral, symmetrical, superior subluxation commonly found in Marfan's syndrome or homocystinuria). It is sometimes associated with ectopic pupils and keratoconus. Unless there are complications (e.g. secondary glaucoma) or monocular diplopia the lens is left in place and management is optical. (Fig. L21) See corectopia; iridodonesis; pupillary block.
Fig. L21 Dislocation of the lens (usually in the vitreous humour)enlarge picture
Fig. L21 Dislocation of the lens (usually in the vitreous humour)

ec·to·pi·a len·tis

(ek-tō'pē-ă len'tis) [MIM*225100]
Displacement of the lens of the eye.

ectopia lentis,

n a displacement of the lens of the eye.

ectopia

[L.] ectopy.

ectopia cordis
congenital displacement of the heart outside the thoracic cavity.
ectopia lentis
congenital displacement of the lens away from its usual site attached to the ciliary body. Occurs as one of a series of defects in an inherited syndrome of cattle. The other defects are irideremia, microphakia and cataract. The calves are normal in other respects.
References in periodicals archive ?
Surgical management of ectopia lentis is a challenge to an eye surgeon.
Lensectomy followed by aphakic spectacles is safe but not an ideal treatment option to manage ectopia lentis in pediatric eyes.
We believe that management of ectopia lentis using a modified CTR and primary implantation of a rigid IOL in the capsular bag gives good visual outcome with no serious complications.
Visual outcome and complications in surgery for ectopia lentis in children.
All patients with unexplained ectopia lentis should be screened for homocystinuria.
Before the Johns Hopkins report, it was widely assumed that someone with ectopia lentis and long extremities almost certainly had Marfan syndrome.
The other group consisted of people initially thought to have Marfan syndrome; however, this group did not meet the diagnostic criteria because they had minimal or no aortic enlargement, no dissection, no ectopia lentis and no family history of Marfan syndrome.
For several decades this disorder was mistaken for Marfan syndrome because of the following similar characteristics: ectopia lentis, excessive height, dolichostenomelia, scoliosis and anterior chest deformities.
They develop scoliosis over time, but do not develop ectopia lentis.
There are also screening exams for the manifestations of Marfan syndrome, such as the slit-lamp examination for ectopia lentis, AP pelvic radiographs for protrusio acetabulae and CTA of the aorta.