Of these patients, 5 had a duodenal atresia (DA), 3 a duodenal web, and 2 an extrinsic obstruction (an annular pancreas with a complete obstruction of the lumen and a preduodenal portal vein with a quite complete obstruction).
Several techniques have been described for the repair of duodenal atresia. Prior to the mid-1970s duodenojejunostomy was the preferred technique followed by side-to-side duodenoduodenostomy, partial web resection with Heineke-Mikulicz type duodenoplasty, and tapering duodenoplasty.
Once the clotting profile and anaemia had been stabilised by multiple transfusions of fresh frozen plasma (FFP), cryoprecipitate, packed red-blood cells (PRBC), platelets and Factor IX, a laparotomy was performed for
duodenal atresia and for a duodenostomy when the baby was 4 weeks of age.
The second patient, born with a hypoplastic left heart and aortic coarctation, died of uncontrollable pulmonary hypertension shortly following an open
duodenal atresia repair.
In conclusion,
duodenal atresia and situs inversus are rare combinations.
Duodenal atresia 4 19 18.27% Oesophageal atresia 1 Cleft lip 5 TEF 2 CDH 2 Cleft palate 2 Ileal atresia 1 4.
CDS is a relatively rare condition in comparison with congenital
duodenal atresia [4].
Differential diagnosis of this sign, detected either prenatally or postnatally, includes
duodenal atresia, annular pancreas, duodenal stenosis, duodenal webs, and midgut volvulus.
PDPV is rarely an isolated incident associated with Situs inversus or heterotaxia or with associated cardiac anomalies, asplenia or poly splenia, biliary atresia,
duodenal atresia, malrotation.
Recently CHAOS has been described as part of a newly proposed association, TACRD (Tracheal Agenesis, complex congenital Cardiac abnormalities, Radial ray defects, and
duodenal atresia) pattern.
Single umbilical artery 3 Congenital diaphragmatic hernia 3 Renal anomalies 4
Duodenal atresia 1 Cystic hygroma 1 Dandy walker cyst 1 Sacral meningomyelocele 1 Gastroschisis 1 Others include 1 patient with absent diastolic flow in umbilical arteries and 1 patient with high resistance to flow in uterine arteries.
