ductal plate malformation

ductal plate malformation

Malformation consisting of congenital hepatic fibrosis with probable autosomal recessive inheritance.
See also: dysencephalia splanchnocystica.
References in periodicals archive ?
Fibrocystic changes to the liver are possibly the only other constant finding [33% to 100%], typically manifesting as impeded development of the intrahepatic biliary system and ductal plate malformation.
Ductal plate malformation results from persistence or absence of remodeling of the embryonic ductal plate during ontogenesis.
Also known as von Meyenburg complexes, bile duct hamartomas arise from ductal plate malformations that involve the small interlobular bile ducts.