Double outlet right ventricle (DORV) is a group of complex congenital heart abnormalities, in which both the pulmonary artery and the aorta arise primarily from the right ventricle.
Double outlet right ventricle type, surgical procedure, and outcome
Surgical outcomes of 380 patients with double outlet right ventricle who underwent biventricular repair.
Indications included pulmonary atresia with ventricular septal defect (VSD) in 11 patients, Tetralogy of Fallot (ToF) with absent pulmonary valve syndrome (APVS) in 2 patients, double outlet right ventricle (DORV), transposition of great arteries (TGA) and pulmonary stenosis in 1 patient each, an infected pseudo-aneurysm in 1 patient and aortic valve disease needing a Ross procedure in 1 patient.
MAPCAS= major aorto-pulmonary collateral arteries, PDA= patent ductus arteriosus, PFO= patent foramen ovale, TGA= transposition of great arteries, VSD= ventricular septal defect, DORV= Double outlet right ventricle, RV= right ventricle, PA= pulmonary artery.
PA; pulmonary atresia, VSD; ventricular septal defect, DORV; double outlet right ventricle, TGA; transposition of great arteries, APVS; absent pulmonary valve syndrome.