FD is also associated with white matter lesions, and vertebrobasilar artery dolichoectasia (7, 8).
Vertebrobasilar dolichoectasia in Fabry Disease: the earliest marker of neurovascular involvement?
The high incidence of dolichoectasia suggests a higher propensity to atherosclerotic cerebrovascular disease.
Cardiovascular risk and neuroradiological profiles in asymptomatic vertebrobasilar dolichoectasia. Cerebrovasc.
Less common causes of TN caused by vascular compression of the cisternal segment of CN V include saccular aneurysm, arteriovenous malformation, vertebrobasilar dolichoectasia
, dural arteriovenous fistula, and persistent trigeminal artery (1-3).
An MRI/MRA head to pelvis was performed which demonstrated dolichoectasia
of the internal carotid and left vertebral arteries, tortuosity of vessels within the chest, particularly vessels arising from the aortic arch, high-grade stenosis at the origins of the right common carotid and right subclavian arteries and proximal left common carotid artery, marked pectus deformity (Haller index of 13.4) causing compression of the right atrium and leftward shift of heart, and lastly a mildly tortuous left renal artery.
A hormonal influence on the incidence of aneurysm formation is supported by the fact that the greatest incidence of adenoma-associated aneurysms occurs in the context of acromegaly (50%) (1), with associated increased insulin-like growth factor--1 potentially playing a role in the formation of intracranial aneurysms, as well as the more diffuse vasculopathic changes that can be seen in these patients, to include widespread cerebrovascular dolichoectasia
of Cases Acoustic schwannoma 42 Ependymoma 1 Meningioma 6 Epidermoid 4 Arachnoid cyst 5 Lipoma 2 Vertebrobasilar dolichoectasia
2 Figure 2.
In our study group, we demonstrated fenestration of the basilar artery in 2 cases, fenestration of the left PCA in 1 case, dolichoectasia
of the basilar artery in 14 cases, and vertebral/basilar artery indentation to the Bulbus/Pons in 16 cases.
We report a case of vertebro-basilar dolichoectasia
in a 34 year old male patient who presented with sudden onset of headache, dizziness, diplopia and weakness of the left side of the body.
Intracranial arterial dolichoectasia
in autosomal dominant polycystic kidney disease.
Downbeat nystagmus and dolichoectasia
of the vertebrobasilar artery.