desmoplastic small cell tumor

desmoplastic small cell tumor

a high-grade malignant tumor found most often in the abdomen of male adolescents; typically tumor cells contain both desmin and keratin, that is, show hybrid features like fetal mesothelial cells; the exact nature of these cells remains unknown.

des·mo·plas·tic small cell tu·mor

(des'mō-plas'tik smawl sel tū'mŏr)
A high-grade malignant tumor found most often in the abdomen of adolescent males; typically tumor cells contain both desmin and keratin, i.e., show hybrid features such as fetal mesothelial cells; the exact nature of these cells remains unknown.
References in periodicals archive ?
Crombleholme, "Desmoplastic small cell tumor: a report of three cases and a review of the literature," Journal of Pediatric Hematology/Oncology, vol.
Mackay, "Intra-abdominal desmoplastic small cell tumor: a light microscopic, immunocytochemical, ultrastructural, and flow cytometric study," Human Pathology, vol.
Rosai, "Desmoplastic small cell tumor with divergent differentiation," Pediatric Pathology, vol.
Rosai, "Desmoplastic small cell tumor with multi-phenotypic differentiation," Zentralblatt fur Pathologie, vol.
(3,10) Other tumors in which CD99 expression has been reported include synovial sarcomas, desmoplastic small cell tumors, clear cell RCC of the kidney, and rhabdomyosarcomas.