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Spagnoli, "Myxoid dermatofibrosarcoma protuberans
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(DFSP) is a locally aggressive soft tissue neoplasm with intermediate malignant potential, regarded as a low grade sarcoma by the WHO classification of tumours of the skin.
A clinical diagnosis of dermatofibrosarcoma protuberans
(DFSP) is a rare dermal malignancy affecting the deep dermis and subcutaneous tissues.
(3-9) Clinical differential diagnosis includes the nodular variant of chromoblastomycosis, keloids, xanthomas, fibromas, Kaposi's sarcoma, neurofibromas and dermatofibrosarcoma protuberans
. Differentiation of keloidiform lesions on the ears from lepromatous leprosy is difficult, but the unilaterality is characteristic of lobomycosis.
It differs from other fibrous conditions such as fibromatosis, juvenile aponeurotic fibroma, subepidermal nodular fibrosis, and dermatofibrosarcoma protuberans
. (6) The histologic differential diagnosis includes benign tumors such as fibrous histiocytomas, pyogenic granulomas, peripheral nerve sheath tumors, and cutaneous smooth-muscle tumors.
Diferenciar con Fibroma, Queloide, Tumor fibroso recurrente de la infancia, Dermatofibrosarcoma protuberans
, Dedos supranumerarios, cuerno cutaneo o verruga vulgar, Fibroqueratoma periungueal adquirido fibromatosis digital infantil, poroma ecrino, granuloma piogenico.
A chest computed tomography scan is routinely used to look for metastases, but it is not appropriate in sarcomas that rarely metastasise, such as dermatofibrosarcoma protuberans
FNAC of dermatofibrosarcoma protuberans
cases showed scanty to moderate cellularity, consisting of small cohesive clusters of short spindle cells and a diagnosis of BML was given.