Dentatorubral-pallidoluysian atrophy | definition of dentatorubral-pallidoluysian atrophy by Medical dictionary
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a hereditary disorder [MIM#125370] common in Japan that manifests itself with progressive ataxia, myoclonus, seizures, and cognitive impairment; due to abnormal CAG repeats on chromosome. The gene locus is 12p13.31.
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Dentatorubral-pallidoluysian atrophy CAG trinucleotide repeats analysis
Unstable expansion of CAG repeat in hereditary dentatorubral-pallidoluysian atrophy (DRPLA).
We use silver staining  of PCR products to detect expanded CAG trinucleotide repeats in other diseases as well, specifically, spinal bulbar muscular atrophy (expanded repeat length range 40-62), spinal cerebellar ataxia type I (40-82), and dentatorubral-pallidoluysian atrophy