cryptogenic fibrosing alveolitis


Also found in: Acronyms.

id·i·o·path·ic pul·mo·nar·y fi·bro·sis (IPF),

[MIM*178500]
an acute to chronic inflammatory process or interstitial fibrosis of the lung of unknown etiology. seen in association with collagen-vascular diseases.

id·i·o·path·ic pul·mo·nar·y fi·bro·sis

(IPF) (id'ē-ō-path'ik pul'mŏ-nar-ē fī-brō'sis)
Subacute form also called Hamman-Rich syndrome (q.v.); an acute to chronic inflammatory process of the lungs, the healing stage of diffuse alveolar damage or acute interstitial pneumonia, either idiopathic or associated with collagen-vascular diseases.
Synonym(s): cryptogenic fibrosing alveolitis.

cryptogenic fibrosing alveolitis

A progressive lung disease involving thickening and fibrosis of the walls of the ALVEOLI and large mononuclear cells in the alveolar spaces. As the name implies, the cause is unknown but the condition is believed to be the end stage of a disorder brought about by one of a range of possible factors including exposure to various occupational dusts or volatile solvents, virus infections or genetic influences.
References in periodicals archive ?
In the interview with the Newcastle Chronicle, Caroline said: "Our mother was suffering from a very, very rare lung disease, Cryptogenic Fibrosing Alveolitis.
They noted these findings in cryptogenic fibrosing alveolitis, sarcoidosis, farmer's lung disease, histiocytosis, and also bronchiolitis obliterans organizing pneumonia (BOOP).
Jean Johnston, of Newbrough, near Hexham, died in April last year, from cryptogenic fibrosing alveolitis (CFA), a condition which hits only six in 100,000 people.
Jean Johnston, of Sidgate, Newbrough, near Hexham, died in April, aged 68, from cryptogenic fibrosing alveolitis (CFA), a condition which hits only six in 100,000 people.