coproporphyrinogen oxidase

Also found in: Acronyms.

cop·ro·por·phy·rin·o·gen ox·i·dase

an enzyme that catalyzes a step in porphyrin biosynthesis, reacting coproporphyrinogen III and O2 to form protoporphyrinogen IX and 2CO2. A deficiency of this enzyme will result in hereditary coproporphyria.
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References in periodicals archive ?
The association between genetic polymorphisms of coproporphyrinogen oxidase and an atypical porphyrinogenic response to mercury exposure in humans.
The excessive urinary coproporphyrin excretion cannot be caused by an enzymatic deficiency, because coproporphyrinogen oxidase activity was within reference values.