congenital hydrocephalus


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con·gen·i·tal hy·dro·ceph·a·lus

hydrocephalus due to a developmental defect of the brain.

congenital hydrocephalus

Hydrocephalus occurring in newborns, typically caused by birth defects such as spina bifida, aqueductal stenosis, or birth trauma with ventricular hemorrhage.

In congenital hydrocephalus, the faulty drainage of CSF from the ventricles of the brain often results in rapidly increasing head circumference, malformation of the skull (thin bone with widened fontanels and separated sutures), distended scalp veins, thin, shiny scalp skin, weak neck muscles incapable of supporting the head, and abnormal development of psychomotor and cognitive or language skills. In untreated cases of congenital hydrocephalus, the outcome is fatal in about half of the patients due to infection, malnutrition, or increased intracranial pressure. The parents of infants treated neurosurgically for congenital hydrocephalus are instructed in signs and symptoms that may indicate surgical complications: fever and headache, irritability, poor feeding, inconsolability.

See also: hydrocephalus
References in periodicals archive ?
Congenital hydrocephalus is a serious condition that can arise from multiple causes.
Congenital hydrocephalus and ventriculoperitoneal shunts: influence of etiology and programmable shunts on revisions.
The incidence of congenital hydrocephalus and cleft lip with cleft palate decreased significantly from 2003 to 2012.
Since then the charity Research into Congenital Hydrocephalus and other Radical Deformities has benefited from the efforts of Lutterworth GC, who this year raised more than pounds 585.
The most common type of congenital hydrocephalus is aqueductal obstruction or stenosis.
Congenital hydrocephalus is present at birth, while acquired hydrocephalus can develop at the time of birth, but it can also develop at some point afterward.
The surgeons acknowledge they won't know for six months to a year whether Neal suffered any serious brain damage from the condition, known as congenital hydrocephalus.
Examples of disruptions include some types of congenital hydrocephalus; micro-cephaly; bowel atresias (absence or closure of part of the bowel); and limb reduction anomalies (shortened limbs).
The incidence of congenital hydrocephalus is 4 to 10 cases per 100,000 births.[4] In 30% of hydrocephalus cases, stenosis of the cerebral aqueduct is present, and in only 2% of that 30%, the hydrocephalus is due to a trait carried by the female and expressed in the male.
Evaluation of functional outcomes in congenital hydrocephalus. Journal of Paediatric Neurosciences 2011;6(1):4-12.
Congenital hydrocephalus has been described in various animal species including cattle (Sharda and Ingole, 2002), buffalo (Bugalia et al, 1990) mare (Sharma, 1996) and camel (Abubakr et al., 1998).
Prenatal diagnosis in a family with severe type I plasminogen deficiency, ligneous conjunctivitis and congenital hydrocephalus. Prenat Diagn 1999; 19(5): 483-7.

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