congenital hydrocephalus

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con·gen·i·tal hy·dro·ceph·a·lus

hydrocephalus due to a developmental defect of the brain.

congenital hydrocephalus

Hydrocephalus occurring in newborns, typically caused by birth defects such as spina bifida, aqueductal stenosis, or birth trauma with ventricular hemorrhage.

In congenital hydrocephalus, the faulty drainage of CSF from the ventricles of the brain often results in rapidly increasing head circumference, malformation of the skull (thin bone with widened fontanels and separated sutures), distended scalp veins, thin, shiny scalp skin, weak neck muscles incapable of supporting the head, and abnormal development of psychomotor and cognitive or language skills. In untreated cases of congenital hydrocephalus, the outcome is fatal in about half of the patients due to infection, malnutrition, or increased intracranial pressure. The parents of infants treated neurosurgically for congenital hydrocephalus are instructed in signs and symptoms that may indicate surgical complications: fever and headache, irritability, poor feeding, inconsolability.

See also: hydrocephalus
References in periodicals archive ?
Congenital hydrocephalus is present at birth, while acquired hydrocephalus can develop at the time of birth, but it can also develop at some point afterward.
The surgeons acknowledge they won't know for six months to a year whether Neal suffered any serious brain damage from the condition, known as congenital hydrocephalus.
Congenital hydrocephalus affects 1 in 400 infants and many neurosurgeons note that adult or acquired hydrocephalus, which can occur as a result of trauma, the aging process, or disease, is equally represented in their practices.
Prenatal diagnosis in a family with severe type I plasminogen deficiency, ligneous conjunctivitis and congenital hydrocephalus.

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