congenital hydrocephalus


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con·gen·i·tal hy·dro·ceph·a·lus

hydrocephalus due to a developmental defect of the brain.

congenital hydrocephalus

Hydrocephalus occurring in newborns, typically caused by birth defects such as spina bifida, aqueductal stenosis, or birth trauma with ventricular hemorrhage.

In congenital hydrocephalus, the faulty drainage of CSF from the ventricles of the brain often results in rapidly increasing head circumference, malformation of the skull (thin bone with widened fontanels and separated sutures), distended scalp veins, thin, shiny scalp skin, weak neck muscles incapable of supporting the head, and abnormal development of psychomotor and cognitive or language skills. In untreated cases of congenital hydrocephalus, the outcome is fatal in about half of the patients due to infection, malnutrition, or increased intracranial pressure. The parents of infants treated neurosurgically for congenital hydrocephalus are instructed in signs and symptoms that may indicate surgical complications: fever and headache, irritability, poor feeding, inconsolability.

See also: hydrocephalus
References in periodicals archive ?
High incidence of congenital hydrocephalus was seen in multipara females mainly of age group 21-25 years.
Congenital hydrocephalus is a serious condition that can arise from multiple causes.
Congenital hydrocephalus as a rare association with ligneous conjunctivitis and type I plasminogen deficiency.
Congenital hydrocephalus internus and aqueduct stenosis: aetiology and implications for genetic counselling.
A CHARITY competition, in its 44th year, raised pounds 540 for Research in the Congenital Hydrocephalus and other Radical Deformities when it was staged at Lutterworth.
Anaesthetic considerations for congenital hydrocephalus.
Richard stands for Research into Congenital Hydrocephalus and other Radical Deformities (spina-bifida) and this year pounds 787 was raised for the charity.
Congenital Heart Disease 22 Renal anomalies 1 Tracheo-esophageal fistula 2 Hypothyroidism 1 Down's features 26 Cleft lip/palate 6 Primary microcephaly 5 Neural tube defect 8 Congenital heart disease 22 Marfan syndrome 3 Mucopolysaccharidosis 1 Congenital hydrocephalus 1
65 per 10 000 births, congenital hydrocephalus is a common neurological diagnosis in children caused by flow obstruction(s), insufficient drainage or excessive CSF production.
Clinical correlation between congenital hydrocephalus and milestones was also taken into account and it was found that 50% cases with aqueductal stenosis, and all cases of Dandy walker cyst and Arnold Chiari type 2 malformation had delayed milestones.
CASE REPORT: A 15 months old male child had undergone the right sided VP shunt (chhabra - slit in - spring silicone shunt) procedure 13 months back for congenital hydrocephalus.
Children with meningo myelocoele and congenital hydrocephalus may be more susceptible to developing perforation due to weakness in the bowel wall resulting from deficient innervation.

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