Exclusion criteria were recurrent cholesteatoma, having undergone surgery at a different center, less than 2 years of follow-up, having undergone surgery other than a canal wall-down procedure, congenital cholesteatoma
, and residual disease in a short period of time.
and cholesterol granuloma of the temporal bone: role of magnetic resonance imaging.
The patient was diagnosed with an intratympanic membrane congenital cholesteatoma
(CC) can occur in any part of the temporal bone and the commonest site being in the middle ear, most probably due to its early presentation with conductive hearing loss [1, 2].
They discuss anatomical issues that arise, such as labyrinthine fistula and facial nerve dehiscence; controversies in management like the canal wall up versus down debate, facial nerve monitoring, endoscopes, and the value and timing of second-stage surgery; congenital cholesteatoma
; recidivism; and complications of otitis media and cholesteatoma surgery.
Past medical history was remarkable for surgical excision of a congenital cholesteatoma
and insertion of transtympanic tubes to correct a conductive hearing loss.
INTRODUCTION: Congenital cholesteatoma
arises from the embryonic epidermal crest, is a benign Disease with slow progressive growth that destroys neighboring structures, it is considered an epidermal cyst originating from the remnants of squamous keratinized epithelium, the disease may appear in several regions of the temporal bone such as in the middle ear (most frequent site) as well as in the petrous apex, cerebellopontine angle, external acoustic meatus and mastoid process, congenital cholesteatoma
of the mastoid process is the rarest form of presentation in the temporal bone, only 2 to 4% of cholesteatoma presenting to pediatric otologist are congenital in origin.
A congenital cholesteatoma
is defined as a cholesteatoma that sits behind an intact tympanic membrane and is not associated with a history
Only one adult case has been reported in the literature , and congenital cholesteatoma
has been reported only in one case .
CONGENITAL: Cholesteatoma found behind an intact tympanic membrane in a patient with no H/o otitis media is congenital cholesteatoma
. It occurs at five sites in the temporal bone the petrous apex, mastoid, middle ear, middle ear and mastoid and External Auditory canal.
(9) Yamasoba et al proposed that osteoma may be of a congenital nature, based on their reported case of an osteoma that was seen in conjunction with congenital cholesteatoma
. (10) Kaplan et al theorized that a combination of trauma and muscle traction may play a role in the development of osteoma.
The search strategy developed based on MeSH terms identified in the scoping search, cholesteatoma, congenital cholesteatoma
, acquired cholesteatoma, definition, and classification, yielded 6061 references in Medline.