ALG1(redirected from chitobiosyldiphosphodolichol beta-mannosyltransferase)
ALG1A gene on chromosome 16p13.3 that encodes an enzyme that catalyses the first mannosylation step in the biosynthesis of lipid-linked oligosaccharides.
ALG1 is mutated in congenital disorder of glycosylation type Ik (CDGIk).
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