childhood absence epilepsy


Also found in: Dictionary, Thesaurus, Acronyms, Wikipedia.
Related to childhood absence epilepsy: Juvenile Absence Epilepsy

child·hood ab·sence ep·i·lep·sy

[MIM*600131]
a generalized epilepsy syndrome characterized by the onset of absence seizures in childhood, typically at age 6 or 7 years. There is a strong genetic predisposition and girls are affected more often than boys. EEG reveals generalized 3-Hz spike-and-wave activity on a normal background. Prognosis for remission is good if the patient does not also have generalized tonic-clonic seizures.
See also: absence.

child·hood ab·sence ep·i·lep·sy

(chīld'hud ab'sĕns epi-lep-sē)
A generalized epilepsy syndrome characterized by the onset of absence seizures in childhood, typically at age 6 or 7 years. There is a strong genetic predisposition and girls are affected more often than boys. Electroencephalograms reveal generalized 3-Hz spike-wave activity on a normal background. Prognosis for remission is good if the patient does not also have generalized tonic-clonic seizures.
See also: absence
References in periodicals archive ?
(2012) Childhood absence epilepsy. In: Bureau M, Genton P, Dravet C, et al., eds.
The study group enrolled 453 children newly diagnosed with childhood absence epilepsy from July 2004 to October 2007.
Absences occur not only in Childhood Absence Epilepsy were it is the only seizure type of the syndrome, but occur in other types of of idiopathic not localisaton related epilepsy syndromes, like Juvenile Absence Epilepsy (JAE), Juvenile Myoclonic epilepsy (JME) and Eyelid Myoclonia with Absences (Jeavons syndrome).
Although there are some articles related the size of the thalamus is similar or greater in the patients with absence epilepsy than controls, there is also a contrary finding which shows the thalamus size is smaller in childhood absence epilepsy (CAE) patients (3).
(12) Aetiology and syndromic diagnosis are the main predictive factors.9 Recurrence risk is lowest in children with childhood absence epilepsy and benign focal epilepsy of childhood and highest in those with symptomatic seizures or history of Todd's paresis following seizures.(12)
Absence seizures must be the initial and most prominent type of seizure for the diagnosis of childhood absence epilepsy. "By and large, these children are neurologically healthy," Dr.
Of the 58 patients evaluated, 14 were diagnosed with juvenile myoclonic epilepsy, 8 with childhood absence epilepsy, and 36 with generalized tonic-clonic seizures that did not fit the criteria for the previous two syndromes.

Full browser ?