References in periodicals archive ?
Ethylmalonic acid is observed due to defective butyryl-CoA dehydrogenase activity.
Afterwards acetyl-CoAacetoacetyl-CoA and butyryl-CoA are formed from pyruvate as key intermediates in the main branch (Jones and Woods 1986).
De novo synthesis of fatty acid, via acetyl-CoA and butyryl-CoA, is executed by ACACA and FASN (Bionaz and Loor, 2008).