branched-chain ketoaciduria

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Related to branched-chain ketoaciduria: Maple Syrup Urine Disorder


the presence of ketone bodies in the urine; this condition is common in uncontrolled diabetes mellitus but can also occur anytime the body begins to break down fatty tissue to provide energy, as in starvation. Called also ketonuria.
branched-chain ketoaciduria maple syrup urine disease.
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