branched-chain amino acid


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branched-chain amino acid

Any of the amino acids—valine, leucine, isoleucine—that accumulate in maple syrup urine disease, which is due to a deficit in oxidative decarboxylation of the BCAAs keto-acid derivatives.
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Toopcham et al [7] reported that the tripeptide Met-CysSer, containing the branched-chain amino acid Met at the Nterminus, exhibited higher ACE inhibitory activity than that of tetrapeptide Ala-Leu-Ser-Cys.
Isolation and identification of angiotensin I-converting enzyme inhibitory peptides derived from thermolysin-injected beef M. longissimus
It contains readily assimilated proteins originating from milk, in addition to the branched-chain amino acid, L-Leucine.
Vetoquinol USA Launches Rebranded EQUISTRO Product Line
(3) Kim and Lee (2) discussed two studies that reported that ingestion of taurine alone or in combination with branched-chain amino acid (BCCA) was able to reduce DOMS following intense exercise, though it wasn't clear why.
Reducing DELAYED-ONSET MUSCLE SORENESS (DOMS) Through Nutrition
A molecular model of human branched-chain amino acid metabolism.
Liver transplantation from a live donor to a patient with maple syrup urine disease: Two case reports
[3] MSUD is a disorder of branched-chain amino acid catabolism, caused by a deficiency in the branched-chain [alpha]-keto acid dehydrogenase complex, which is responsible for the decarboxylation of the branched-chain amino acids (BCAA), leucine, isoleucine, and valine (Fig.
8-Month-Old Boy with Ataxia after Ingestion of Cow's Milk
Pathway enrichment and topology analysis identified enrichment in purine, pyrimidine, inositol phosphate, and branched-chain amino acid metabolism in addition to lysine degradation in both BMM and MDM.
Transcriptional Profiling Suggests Extensive Metabolic Rewiring of Human and Mouse Macrophages during Early Interferon Alpha Responses
Preexercise branched-chain amino acid administration increases endurance performance in rats.
Physical exercise-induced fatigue: the role of serotonergic and dopaminergic systems
Effects of branched-chain amino acid supplementation after radiofrequency ablation for hepatocellular carcinoma: A randomized trial.
Literature review & commentary
Second, animal protein (high branched-chain amino acid and methionine) consists of meat and dairy, but their fatty acid compositions are quite different.
Study's methodology raises questions
Nguyen et al., "Acrodermatitis enteropathica-like syndrome secondary to branched-chain amino acid deficiency during treatment of maple syrup urine disease," Annales de Dermatologie et de Venereologie, vol.
Skin Lesions Associated with Nutritional Management of Maple Syrup Urine Disease
Formerly, studies have shown that a drop in plasma branched-chain amino acid levels in cases with urea-cycle metabolism disorders can be obtained with sodium phenylacetate/benzoate or sodium phenylbutyrate (NaPB) treatments [4, 5].
A Patient with MSUD: Acute Management with Sodium Phenylacetate/Sodium Benzoate and Sodium Phenylbutyrate
Cardile et al., "Branched-chain amino acid supplementation promotes survival and supports cardiac and skeletal muscle mitochondrial biogenesis in middle-aged mice," Cell Metabolism, vol.
Amino Acid Catabolism in Alzheimer's Disease Brain: Friend or Foe?

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