bile duct hamartoma

bile duct hamartoma

A benign developmental lesion(s) of the liver located in the periportal tract, which may be associated with cavernous haemangiomas, cholangiocarcinoma and autosomal dominant polycystic kidney disease.
References in periodicals archive ?
3) Bile duct hamartoma or von Meyenburg complex is a type of ductal malformation that often occurs sporadically or as part of the spectrum of polycystic liver disease.
Autosomal dominant polycystic liver disease is part of the spectrum of fibropolycystic liver diseases that are caused by congenital bile duct malformation, including bile duct hamartoma, Caroli's disease, congenital hepatic fibrosis, and choledochal cyst.
Also known as von Meyenburg complexes, bile duct hamartomas arise from ductal plate malformations that involve the small interlobular bile ducts.
Bile duct hamartomas (Von Meyenburg complexes): Value of MR imaging in diagnosis.
AC indicates adenocarcinoma; CIS, carcinoma in situ; in situ; and BDH, bile duct hamartoma.
Cholangiocarcinoma arising in bile duct adenoma with focal area of bile duct hamartoma.
This leads to different congenital bile duct disorders, such as Caroli disease and syndrome, autosomal recessive polycystic kidney disease, autosomal dominant polycystic kidney disease, congenital hepatic fibrosis, and bile duct hamartomas (BDHs, also known as von Meyenburg complexes).
Cysts and bile duct hamartomas are hypointense in T1 and hyperintense in T2; they are differentiated by a thin ring of gadolinium enhancement, hemangiomas are more common in women, they are hypointense in T1 and moderately hyperintense in T2, with a centripetal enhancement in the arterial phase.