benign familial chronic pemphigus


Also found in: Acronyms.

be·nign familial chron·ic pem·phi·gus

[MIM*169600]
recurrent eruption of vesicles and bullae that become scaling and crusted lesions with vesicular borders, predominantly of the neck, groin, and axillary regions; autosomal dominant inheritance, presenting in late adolescence or early adult life.

benign familial chronic pemphigus

Etymology: L, benedicere, to bless, familia, household; Gk, pemphix, bubble
a hereditary condition of the skin characterized in the early stages by blisters that break, leaving red, eroded areas followed by crusts. It most commonly occurs on the neck, groin, and axillary regions. It presents in late adolescence or early adulthood. Also called Hailey-Hailey disease.
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Benign familial chronic pemphigus

Hailey,

Hugh Edward, U.S. dermatologist, 1909–.
Hailey-Hailey disease - recurrent eruption of vesicles and bullae. Synonym(s): benign familial chronic pemphigus

Hailey,

William Howard, U.S. dermatologist, 1898-1967.
Hailey-Hailey disease - recurrent eruption of vesicles and bullae. Synonym(s): benign familial chronic pemphigus
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