beta-aminoisobutyrate:pyruvate aminotransferase(redirected from b-aminoisobutyratepyruvate aminotransferase)
β-a·mi·no·i·so·bu·ty·rate:py·ru·vate a·mi·no·trans·fer·ase(ă-mē'nō-ī'sō-bū'ti-rāt pī-rū'vāt ă-mē'nō-tranz'fĕr-ās),
β-Aminosiobutyrate:pyruvate transaminase; an enzyme that catalyzes the reversible transfer of an amino group from β-aminoisobutyrate to pyruvate, producing l-alanine and methylmalonate semialdehyde; a step in valine degradation. A deficiency of this enzyme results in hyper-β-aminoisobutyric aciduria.
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