syndrome seen in patients who have no functional spleen, either because of surgical removal or disease (for example, sickle cell anemia); includes increased susceptibility to bacterial infection, especially of the pneumococcal type.
Ivemark syndromeA heterotaxy syndrome (OMIM:208530) in which both right and left atria of the heart are morphologically right. Other associated anomalies include asplenia, mid-line liver, small intestine malrotation and two morphological right lungs.
In keeping with congenital heart defect—i.e., cyanosis, breathlessness, lethargy, poor feeding.
A rare disorder of fetal development that occurs before the fifth gestational week and results in congenital anomalies of the left hemibody, including absence of the spleen.