apical hypertrophic cardiomyopathy

An uncommon variant of hypertrophic cardiomyopathy (HCM), which is characterised by myocardial hypertrophy, predominantly in the left ventricular apex, which constitutes up to 25% of all HCM in Japan, but less than 5% of non-Japanese populations.
Associations, apical HCM Sudden cardiac death, severe arrhythmias, and apical infarctions with apical aneurysms, imparting a “spade-shaped” configuration of the LV cavity at end-diastole on ventriculography and “giant” T-wave negativity in the EKG.
Diagnosis Echocardiography, cardiac MRI should be performed if EKG raises suspicion of apical HCM.

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giant T wave inversion

References in periodicals archive ?

Yamaguchi syndrome, or apical hypertrophic cardiomyopathy (ApHCM), is a nonobstructive subtype of hypertrophic cardiomyopathy which predominantly affects the left ventricular apex.

Apical hypertrophic cardiomyopathy (ApHCM) is a nonobstructive and relatively rare subtype of hypertrophic cardiomyopathy (HCM).

Yamaguchi syndrome - A pseudoacute coronary syndrome of the young: A case report on apical hypertrophic cardiomyopathy

Apical hypertrophic cardiomyopathy associated with multiple coronary artery-left ventricular fistulae: a report of a case and review of the literature.

Case Report: Unusual cause of chest pain in an elderly male

Apical hypertrophic cardiomyopathy (HCM) is one of the rare cardiomyopathies which can also present like an acute myocardial infarction (MI).

A 66-Year-Old Female with Apical Hypertrophic Cardiomyopathy Presenting with Hypertensive Crises and Type 2 Myocardial Infarction and a Normal Coronary Angiogram

Apical Hypertrophic Cardiomyopathy (AHCM) is a rare form of Hypertrophic Cardiomyopathy (HCM), which usually involves the apex of the left ventricle and rarely involves the right ventricular apex or both.

Case report--isolated apical hypertrophic cardiomyopathy

"Further tests done have revealed he is suffering from an apical hypertrophic cardiomyopathy (HCM)."

Former Arsenal Shot-Stopper Manuel Almunia Forced To Leave Football After Heart Problem Discovery

Two-dimensional transthoracic echocardiography showed typical of apical hypertrophic cardiomyopathy (AHCM) without regional wall motion abnormality and with normal left ventricular systolic function (Fig.

Coronary artery-left ventricular microfistulas associated with apical/Hypertrophic cardiomyopathy koroner arter-sol ventrikul arasindaki mikrofistullerin apikal hipertrofik kardiyomiyopati ile birlikteligi

Advances in diagnostic imaging modalities have undoubtedly led to an increase in detection of this rare condition and it is likely that earlier cases have been misdiagnosed as phenotypically similar cardiomyopathies, such as apical hypertrophic cardiomyopathy [9], where prognosis and treatment may differ significantly.

Non-compaction cardiomyopathy in an apparently healthy patient: a case report

She had multiple lentigines, cardiac anomalies (apical hypertrophic cardiomyopathy, left ventricular hypertrophy and pulmonary stenosis), ocular hypertelorism and abnormal electrocardiographic findings.

A rare cause of dyspnoea: the LEOPARD syndrome

Correlation between left ventricular wall thickness and the depth of negative T waves in apical hypertrophic cardiomyopathy J Cardiogr 1984; 14: 281-8.

Japanese type cardiomyopathy without deep negative T-waves and with findings of preexcitation on EGG/EKG'de derin negatif T dalgalan izlenmeyen, preeksitasyon bulgulari izlenen Japon tipi kardiyomiyopati

Comparison of prevalence of apical hypertrophic cardiomyopathy in Japan and the United States.

Hypertrophic cardiomyopathy and the Hypertrophic Cardiomyopathy Association/Hipertrofik kardiyomiyopati ve Hipertrofik Kardiyomiyopati Dernegi

Apical hypertrophic cardiomyopathy presenting with sustained monomorphic ventricular tachycardia and electrocardiographic changes simulating coronary artery disease and left ventricular aneurysm.

Hypertrophic cardiomyopathy with massive midventricular hypertrophy, midventricular obstruction and an akinetic apical chamber/Akinetik apikal bosluk, midventrikuler obstruksiyon ve midventrikuler hipertrofi ile seyreden hipertrofik kardiyomiyopati