aortoventricular tunnelA rare (circa 0.25% of congenital heart malformations) “congenital extracardiac channel that connects the ascending aorta above the sinutubular junction to the cavity of the left (or, less commonly, right) ventricle, which may be accompanied by defects of the proximal coronary arteries or aortic or pulmonary valves” (R McKay, 2005). While patients with small channels may present with asymptomatic heart murmurs and cardiac enlargement, most suffer heart failure in the first year of life.
Management Prompt surgical repair.
Segen's Medical Dictionary. © 2012 Farlex, Inc. All rights reserved.