Paraganglia in the head and neck region (Including aorticopulmonary
paraganglia), which are in close alignment with the parasympathetic nervous system,
Therefore, MRI provides more accurate results especially in the assessment of hilar and aorticopulmonary
lymph nodes (3).
Abnormal cusp formation results either from aberrant fusion of the aorticopulmonary
septum or from abnormal mesenchymal proliferation in the common trunk, clinically leading to a severe regurgitation [4, 10].
 ARSCA was more common in female than in male and commonly seen in disorders such as Down syndrome, DiGeorge and Edward's syndromes, tetralogy of Fallot, pulmonary atresia, or major aorticopulmonary
They participate in the formation of aorticopulmonary
septum, the tunica media of the great arteries, the outflow tract septum, and the semilunar valves,[sup],,,, throughout the embryonic development.
Mediastinal paragangliomas are hypervascular tumours and many of them invade or firmly adhere to the adjacent mediastinal organs such as heart, great vessels, trachea and the spine.1 Mediastinal paragangliomas are predominantly concentrated in two locations; the aorticosympathetic paraganglia of the posterior mediastinum or the autonomic ganglia in the superior and middle mediastinum.6 Aorticopulmonary
tumours tend to occur in patients with a mean age of 49 years with no gender preference and only 3% of these secrete catecholamines.
A second classification system was later described primarily based on the presence (type A) or absence (type B) of a VSD and development of the aorticopulmonary
Therefore, secondary evidence of partial absence of the left pericardium is key in confirming the diagnosis such as excessive leftward deviation of the cardiac apex and lung interposed between the heart and diaphragm as well as lung extending between the aorta and pulmonary artery in the aorticopulmonary
window, a finding considered pathognomonic for this condition (Figure 14).
 the incidence of the aberrant subclavian artery was 6% in patients with the tetralogy of Fallot and 16% with its combination and pulmonary atresia or major aorticopulmonary
Resection of parathyroid tumor in the aorticopulmonary
window without prior neck exploration.
The absence of certain signs may help in excluding the diagnosis: loss of the aorticopulmonary
window, abnormality of the aortic arch, rightward tracheal shift, and widening of the left paraspinal line without associated fracture.
Eisenmenger syndrome consists of pulmonary hypertension due to high pulmonary vascular resistance with reversed or bidirectional shunts at the aorticopulmonary
, ventricular, or atrial levels (1).