Also found in: Acronyms, Wikipedia.
a benign tumor containing vascular, adipose, and muscle elements, occurring most often in the kidney with smooth muscle elements.
A benign neoplasm of adipose tissue (lipoma) in which muscle cells and vascular structures are fairly conspicuous; most commonly a renal tumor containing smooth muscle, often associated with tuberous sclerosis.
[angio- + G. mys, muscle, + lipos, fat, + -oma, tumor]
A benign tumor composed of adipose tissue, muscle cells, and vascular structures.
angiomyolipomaA benign, well-circumscribed, nonencapsulated tumour-like lesion or hamartoma (perivascular epithelioid cell tumour—PEComa), which is the most common mesenchymal lesion of the kidney. It is composed of blood vessels, smooth muscle and mature fat, and is typically seen in the kidney or paranephric tissue. Angiomyolipoma also occurs in the fallopian tube, liver, nasal cavity, penis, skin, spermatic cord and vagina, and can mimic renal cell carcinoma. Up to 50% of patients have tuberous sclerosis (TS); 75% of TS patients have angiomyolipomas.
May cause catastrophic bleeds.
TSC1 and TSC2 mutations.
A benign neoplasm of adipose tissue (lipoma) in which muscle cells and vascular structures are fairly conspicuous.