pulmonary glomangiosis

(redirected from angiomatoid lesion)

pul·mo·nar·y glo·man·gi·o·sis

glomangiosis occurring within small pulmonary arteries in severe pulmonary hypertension and congenital heart disease.

plexiform lesion of the lung

A lesion that is the histopathologic hallmark of pulmonary arterial hypertension, which consists of obliterative endothelial cell proliferation and vascular smooth muscle cell hypertrophy in small precapillary pulmonary arterioles.
References in periodicals archive ?
When arterial branch dilatation affects a cluster of vessels, it is termed an angiomatoid lesion Grade V (hallmark Plexiform Plexus of lesion) proliferation capillary-like channels within a dilated arterial branch of the thick-walled parent artery that yields a glomoid appearance to the vessel + overlying thrombotic material Grade VI (rare) Vascular necrosis + Fibrinoid necrosis inflammation of smooth muscle in the vascular media + a necrotizing arteritis with either lymphocytes or neutrophils
ABH has to be differentiated from blood dyscrasias (thrombocytopenia, von Willebrand's disease, other coagulopathies and leukemia), immunobullous disorders (bullous pemphigoid, linear IgA disease, cicatricial pemphigoid, and dermatitis herpetiformis), angiomatoid lesions in Osler-Rendu-Weber syndrome.