angioimmunoblastic lymphadenopathy

(redirected from angioimmunoblastic lymphoma)

lymphadenopathy

 [lim-fad″ĕ-nop´ah-the]
disease of the lymph nodes; called also adenopathy.
angioimmunoblastic lymphadenopathy (angioimmunoblastic lymphadenopathy with dysproteinemia (AILD)) a systemic disorder resembling lymphoma characterized by fever, night sweats, weight loss, generalized lymphadenopathy, hepatosplenomegaly, macropapular rash, polyclonal hypergammaglobulinemia, and Coombs'-positive hemolytic anemia. It is considered to be a nonmalignant hyperimmune reaction to chronic antigenic stimulation; there is proliferation of B cells accompanied by profound deficiency of T cells. The disease follows a progressive but extremely variable course: some patients survive for a long period without chemotherapy; in other patients, overwhelming infections rapidly lead to death
dermatopathic lymphadenopathy regional lymph node enlargement associated with melanoderma and other dermatoses marked by chronic erythroderma.
immunoblastic lymphadenopathy angioimmunoblastic lymphadenopathy.
lymphadenopathy syndrome a condition occurring in immunocompromised individuals, characterized by unexplained lymphadenopathy for 3 or more months that involves extrainguinal sites, which on biopsy reveal nonspecific lymphoid hyperplasia. See also AIDS-related complex.

angioimmunoblastic lymphadenopathy

(1) A condition now subsumed under T-cell lymphoma.
(2) Angioimmunoblastic lymphadenopathy with dysproteinaemia.
References in periodicals archive ?
In the present case the background cells were atypical and showed CD3, CD4, CD5, and CD25 phenotypes with a marked reduction of CD7 positivity, as observed in ATLL (1) and were negative for CD10 and PD1 enabling a differential diagnosis with angioimmunoblastic lymphoma, a disease that may also present HRS-like cells.
Patients with Hodgkin-like and pleomorphic small cell types have better survival compared with ALCL and angioimmunoblastic lymphoma type.