amylopectinosis


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amylopectinosis

 [am″ĭ-lo-pek´tĭ-no´sis]
glycogen storage disease (type IV), a condition in which deficiency of the brancher enzyme amylo-1:4,1:6-transglucoside results in cirrhosis of the liver, hepatosplenomegaly, and progressive hepatic failure and death. Called also Andersen's disease.