amelogenesis imperfecta


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Related to amelogenesis imperfecta: dentinogenesis imperfecta

amelogenesis

 [ah-mel″o-jen´ĕ-sis]
formation of dental enamel.
amelogenesis imperfec´ta a hereditary disease in which there is imperfect formation of enamel, resulting in brownish coloration and friability of the teeth.

am·e·lo·gen·e·sis im·per·fec·ta

a group of hereditary ectodermal disorders in which the enamel is defective in structure or deficient in quantity. Three major groups are recognized: hypoplastic types, with defective enamel matrix deposition but normal mineralization; hypomineralization types, with normal matrix but defective mineralization; and hypomaturation type, in which the enamel crystallites remain immature. The several types may be inherited as autosomal dominant [MIM*104500, 104510, 104530], recessive [MIM*204650, 204690, 204700] or X-linked [MIM*301100, 301200, 301201].

amelogenesis imperfecta

(ĭm′pər-fĕk′tə)
n.
A hereditary condition in which the dental enamel does not develop properly, often because of insufficient calcification.

amelogenesis imperfecta

a condition characterized by brown or white chalky discoloration of the teeth and resulting from either severe enamel hypocalcification or enamel hypoplasia. The condition, which is inherited as an autosomal-dominant trait, is classified according to severity: in agenesis, there is a complete lack of enamel; in enamel hypoplasia, defective matrix formation causes the enamel to be normal in hardness but deficient in quantity; and in enamel hypocalcification, defective maturation of ameloblasts results in enamel that is normal in quantity but soft and undercalcified. Also called hereditary brown enamel,hereditary enamel hypoplasia.Compare dentinogenesis imperfecta.

am·e·lo·gen·e·sis im·per·fec·ta

(amĕ-lō-jenĕ-sis im-pĕr-fektă)
Hereditary ectodermal disorders in which dental enamel is defective in structure or deficient in quantity.

amelogenesis imperfecta

A hereditary defect of the mineralization of tooth enamel which is unusually soft and is rapidly worn away.

am·e·lo·gen·e·sis im·per·fec·ta

(amĕ-lō-jenĕ-sis im-pĕr-fektă)
Group of hereditary ectodermal disorders in which tooth enamel is defective in structure or deficient in quantity. Three major groups are recognized.
Synonym(s): enamel dysplasia.

amelogenesis imperfecta (am´əlōjen´əsis),

n a broad category of developmental disturbances in the structural formation of enamel. The disease is divided into four main types (type 1, Hypoplastic; type 2, Hypomaturation; type 3, Hypocalcified; type 4, mixed) and 15 subtypes, which range from mild to severe.
Enlarge picture
Amelogenesis imperfecta.

amelogenesis

formation of dental enamel.

amelogenesis imperfecta
imperfect formation of enamel, resulting in brownish coloration and friability of the teeth.
References in periodicals archive ?
An interdisciplinary approach for restoring function and esthetics in a patient with amelogenesis imperfecta and malocclusion: a clinical report.
MMP-20 mutation in autosomal recessive pigmented hypomaturation amelogenesis imperfecta.
Enamelin and Autosomal-dominant Amelogenesis Imperfecta.
Sundell S, Valentin J (1986) hereditary aspects and classification of hereditary amelogenesis imperfecta.
Interdisciplinary treatment of a patient with amelogenesis imperfecta, a skeletal class III relationship, and an anterior open bite.
El tratamiento para los pacientes con amelogenesis imperfecta depende de varios factores que se deben considerar como la edad, el tipo y el grado de severidad de la afeccion, la situacion intraoral y el estado socioeconomico.
Some oro-dental findings, such as congenitally missing teeth, amelogenesis imperfecta or cleft of the lip and palate, may be isolated defects.
The treatment for patients with amelogenesis imperfecta is related to many factors including the age of patients, the socio-economic status, the type and severity of the disorder, its intra oral manifestation and aesthetic and functional demands.
La extraccion del primer molar permanente es una buena opcion de tratamiento de ortodoncia en los casos donde estos dientes estan muy destruidos por caries extensas, amelogenesis imperfecta, restauraciones grandes mal adapatdas, etc.
This clinical report describes the prosthodontic treatment for a 28-year-old male diagnosed with Type 1 hypoplastic amelogenesis imperfecta.
The researchers say a determination of the gene's exact location should boost their understanding of a rare, hereditary weakness of tooth enamel called amelogenesis imperfecta.
Clinical Characteristics of Tooth Decay in Individuals with Different Amelogenesis Imperfecta Phenotypes