aggressive angiomyxoma

aggressive angiomyxoma

locally invasive, but nonmetastasizing tumor of genital organs in young women.

Aggressive Angiomyxoma

A rare, locally aggressive, non-metastasising tumour of the vulva, vagina, pelvis and/or perineum, usually of pre-menopausal women. In the vulva, it presents as a firm, rubbery subcutaneous mass, often near Bartholin’s gland, and may be misdiagnosed as a Bartholin’s gland cyst.
Management Wide local excision without lymphadenectomy.
Prognosis Late recurrence occurs in 35–72%; no metastases have been reported.

ag·gres·sive an·gi·o·myx·o·ma

(ă-gres'iv an'jē-ō-miks-ō'mă)
Locally invasive, but nonmetastasizing tumor of genital organs in young women.
References in periodicals archive ?
Aggressive angiomyxoma may commonly mimic ovarian myxoma both with immunohistochemical and ultrastructural findings.
in 1992 as an important distinction from aggressive angiomyxoma (AA), which is an infiltrative myxedematous mesenchymal tumor with the potential for local recurrence [7].
The medical literature suggests that about 3 out of 10 (30%) aggressive angiomyxoma tumours will come back (recur].
Aggressive angiomyxoma mostly affects women and arises in the perineal and pelvic regions.
On immunohistochemistry both angiomyofibroblastoma-like tumor and aggressive angiomyxoma are positive for Desmin and SMA.
The differential diagnosis of intramuscular myxomas includes also aggressive angiomyxoma, myxoid neurofibroma, myxoid liposarcoma, cellular or juxta-articular myxoma, and nodular fasciitis [18, 19].
Aggressive angiomyxoma (AA) is a rare soft-tissue tumor that is typically found in the perineum of females of reproductive age.
"[Cellular angiofibroma, angiomyofibroblastoma and aggressive angiomyxoma: members of a spectrum of genital stromal tumours?]," Ann Pathol.
The differential diagnosis might include a myxoid tumor such as myxoid neurofibroma or aggressive angiomyxoma due to the presence of myxoid, proteinaceous, or mucinous contents.
Cellular angiofibroma can also be confused with aggressive vulvo-vaginal tumours like aggressive angiomyxoma and solitary fibrous tumour (1, 5).
Aggressive angiomyxoma is a rare, myofibroblastic tumour, of pelvi-perineum of young women.