adult rhabdomyoma

adult rhabdomyoma

A rare, usually benign primary (extracardiac) striated muscle tumour (or tumours—multiple in 20% of cases) that arises in branchial arches III and IV of the head and neck (larynx, pharynx). It is more common in males > age 40.

Prognosis
May recur; 1:50 are malignant.
References in periodicals archive ?
Hyams, "Adult rhabdomyoma of the head and neck: a clinicopathologic and immunophenotypic study," Human Pathology, vol.
Mestdagh, "Adult rhabdomyoma of the larynx," Archives of Oto-Rhino-Laryngology, vol.
Bickel, "Multifocal adult rhabdomyoma: a case report and literature review," American Journal of Otolaryngology, vol.
Some authors have highlighted the cytologic resemblance of CSH to the cells of adult rhabdomyoma, a tumor that has not yet been described in the lung and therefore is an unlikely diagnostic problem in pulmonary pathology.
Crystal-storing histiocytosis associated with lymphoplasmacytic neoplasms: report of three cases mimicking adult rhabdomyoma. Am J Surg Pathol.
Hyderabad, Andhra Pradesh, August 29, 2011 /India PRwire/ - Prime Hospitals, with two full fledged, multi-speciality branches in Hyderabad (Ameerpet and Kukatpally) with a cumulative bed strength of 300, makes the city of Hyderabad proud by doing a rare surgery - Adult Rhabdomyoma surgery, on a 25 year old male patient.
We report a case of adult rhabdomyoma of the larynx that features some of its typical and atypical presenting characteristics.
In this article, we report a case of adult rhabdomyoma of the larynx that typified the common indolent progression of dysphagia and dysphonia but featured a more acute presentation of upper airway obstruction.
The differential diagnosis of a cardiac mass with features similar to CSH includes genetic storage disorders, adult rhabdomyoma, Weber-Christian disease, Langerhans cell histiocytosis, Rosai-Dorfman disease, Erdheim-Chester disease, or cardiac inflammatory myofibroblastic tumor.
Immunohistochemistry staining is positive for desmin and vimentin and is less dense for myoglobin than in adult rhabdomyoma. (5)
Histologically, our patient's neoplasm showed the classic features of adult rhabdomyoma: differentiated skeletal muscle composed of large, round to oval cells with pale, pink-staining, finely granular cytoplasm.
Some authors have speculated that extracardiac rhabdomyomas are hamartomas, but recent work by Gibas and Miettinen[11] showed a 15-19 translocation in a recurrent adult rhabdomyoma, making neoplastic transformation more likely.
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