apical hypertrophic cardiomyopathy

(redirected from Yamaguchi syndrome)

apical hypertrophic cardiomyopathy

An uncommon variant of hypertrophic cardiomyopathy (HCM), which is characterised by myocardial hypertrophy, predominantly in the left ventricular apex, which constitutes up to 25% of all HCM in Japan, but less than 5% of non-Japanese populations.
Associations, apical HCM Sudden cardiac death, severe arrhythmias, and apical infarctions with apical aneurysms, imparting a “spade-shaped” configuration of the LV cavity at end-diastole on ventriculography and “giant” T-wave negativity in the EKG.
Diagnosis Echocardiography, cardiac MRI should be performed if EKG raises suspicion of apical HCM.
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As far as we explored, this is the first case report of Yamaguchi Syndrome without deep negative T waves and with findings of preexcitation in literature.

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