West syndrome


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West syn·drome

(west),
an encephalopathy in infancy characterized by infantile spasms, arrest of psychomotor development, and hypsarrhythmia.

West syn·drome

(west),
an encephalopathy in infancy characterized by infantile spasms, arrest of psychomotor development, and hypsarrhythmia.
An early onset condition characterised by a triad:
(1) Infantile spasms,
(2) Interictal EEG pattern termed hypsarrhythmia, and
(3) Mental retardation. Per the international classification, the diagnosis can be made in the presence of two of the three symptoms. The frequent onset of West syndrome in infancy suggests that CNS immaturity may play a key role in its pathogenesis. The clinical response to ACTH and glucocorticoids may be linked to suppression of corticotropin-releasing hormone production

West syndrome

Massive myoclonus Neurology An occasionally X-linked condition characterized by infantile spasms–seizures and 2º generalized epilepsy, hypsarrhythmia, encephalopathy with mental retardation and arrested psychomotor development, ± with immune dysfunction and death at an early age due to bronchopneumonia. See Salaam convulsions.

West syn·drome

(west sin'drōm)
An encephalopathy in infancy characterized by infantile spasms, arrest of psychomotor development, and hypsarrhythmia.

West,

Charles, English physician, 1816-1898.
West syndrome - an encephalopathy in infancy characterized by infantile spasms, arrest of psychomotor development, and hypsarhythmia.
References in periodicals archive ?
Treatment and long term outcome in West syndrome: The clinical reality.
Kain was diagnosed with West syndrome, mental and neurological delay, medically resistant epilepsy and blindness at three months old.
Notably, 7 of 27 children (26%) with West syndrome were misdiagnosed--in six cases with GERD, and in one case with infant colic.
Global Markets Direct's, 'Infantile Spasm (West Syndrome) - Pipeline Review, H1 2016', provides an overview of the Infantile Spasm (West Syndrome) pipeline landscape.
In this article, we report the case of a six-month-old male patient diagnosed with West syndrome associated with vitamin [B.sub.12] deficiency.
A British father of a one-year-old daughter with Infantile Spasms (West Syndrome) - a severe form of epilepsy- is planning to run the Dubai Marathon next year to raise awareness of this rare disability.
For example, the seizure type of the West syndrome, which was considered a generalized epilepsy syndrome, was infantile spasms and EEGs showed generalized spike and wave discharges; however; many infants had a causative focal lesion and their epilepsy had been cured by focal resections.
INTRODUCTION: West syndrome is a rare epileptic disorder in infants, children and adults, characterized by triad of infantile spasm, path gnomic EEG pattern and developmental regression.
Dakota, who did not breathe for the first seven-and-a-half minutes of her life, was born with meningitis, before being diagnosed with cerebral palsy and West syndrome. That is an epileptic condition suffered by only one in 250,000 people.
" Carla also developed West Syndrome at five months old, a rare form of epilepsy in children, which led to majo r setbacks in her development.
Neuroepidemiology of West syndrome and early infantile epileptic encephalopathy in Miyagi Prefecture, Japan.

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