uroporphyrinogen decarboxylase

(redirected from Uroporphyrinogen III decarboxylase)
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ur·o·por·phy·rin·o·gen de·car·box·yl·ase

an enzyme that participates in heme biosynthesis; it catalyzes the decarboxylation of uroporphyrin III to produce coproporphyrinogen III; it also acts on uroporphyrin I; a deficiency of this enzyme will result in either porphyria cutanea tarda or hepatoerythropoietic porphyria.