Summary: Kochi (Kerala) [India] March 28 (ANI/BusinessWireIndia): In a rare surgery, doctors at Aster Medcity have successfully resected last part of colon and rectum of a 43-year-old male patient, who was suffering from Klippel Trenaunay
's Syndrome with intractable rectal bleed, using laparoscopy.
Five syndromes have been reported associated with intestinal lymphangiectasia: von Recklinghausen, Turner or Noonan, Klippel Trenaunay
and Hennekam (4).
syndrome: Spectrum and management.
The French physicians Maurice Klippel and Paul Trenaunay
first described this syndrome in 1900 when they associated vascular malformations with hypertrophy in the affected limb.
The French physicians, Klippel and Trenaunay
, reported the first case in 1900.
In 1900, French physicians, Klippel and Trenaunay
, first described what became known as Klippel-Trenaunay syndrome after two patients presented with a triad of symptoms - port-wine stain, varicose veins, and bony and soft tissue hypertrophy involving an extremity.
The now 40-year-old coach at the University of Oregon, who did come through qualifying, suffers from a birth defect in his right leg known as Klippel Trenaunay
Back, "A case of femoral fracture in klippel trenaunay
syndrome," Case Reports in Orthopedics, vol.
It was described by the French doctors, Maurice Klippel and Paul Trenaunay
, for the first time in 1900s.
(9,10) Rarely, splenic lymphangiomas can be part of Klippel Trenaunay
syndrome (characterized by varicose veins, bony and soft tissue hypertrophy, cutaneous hemangiomas, and/ or malformations of the lymphatic system).
There are also reports claiming minor traumas as a cause of pseudo-Kaposi sarcoma.1 Intractable cutaneous ulcers may complicate Klippel- Trenaunay
syndrome.2 We report a case of Klippel-Trenaunay sundrome with extensive ulcerations developing in the port-wine stain and a solitary pseudo-Kaposi sarcoma.