Summary: Kochi (Kerala) [India] March 28 (ANI/BusinessWireIndia): In a rare surgery, doctors at Aster Medcity have successfully resected last part of colon and rectum of a 43-year-old male patient, who was suffering from Klippel
Trenaunay's Syndrome with intractable rectal bleed, using laparoscopy.
Five syndromes have been reported associated with intestinal lymphangiectasia: von Recklinghausen, Turner or Noonan, Klippel
Trenaunay and Hennekam (4).
Klippel
Trenaunay syndrome: Spectrum and management.
The French physicians Maurice Klippel and Paul
Trenaunay first described this syndrome in 1900 when they associated vascular malformations with hypertrophy in the affected limb.
The French physicians, Klippel and
Trenaunay, reported the first case in 1900[3].
In 1900, French physicians, Klippel and
Trenaunay, first described what became known as Klippel-Trenaunay syndrome after two patients presented with a triad of symptoms - port-wine stain, varicose veins, and bony and soft tissue hypertrophy involving an extremity.
The now 40-year-old coach at the University of Oregon, who did come through qualifying, suffers from a birth defect in his right leg known as Klippel
Trenaunay Weber Syndrome.
Back, "A case of femoral fracture in klippel
trenaunay syndrome," Case Reports in Orthopedics, vol.
It was described by the French doctors, Maurice Klippel and Paul
Trenaunay, for the first time in 1900s.
(9,10) Rarely, splenic lymphangiomas can be part of Klippel
Trenaunay syndrome (characterized by varicose veins, bony and soft tissue hypertrophy, cutaneous hemangiomas, and/ or malformations of the lymphatic system).
There are also reports claiming minor traumas as a cause of pseudo-Kaposi sarcoma.1 Intractable cutaneous ulcers may complicate Klippel-
Trenaunay syndrome.2 We report a case of Klippel-Trenaunay sundrome with extensive ulcerations developing in the port-wine stain and a solitary pseudo-Kaposi sarcoma.