TEMPI syndrome

TEMPI syndrome

A rare syndrome of unknown cause, consisting of telangiectasia, erythrocytosis, elevated monoclonal paraprotein levels, perinephric fluid collections and intrapulmonary shunting.
References in periodicals archive ?
The pathogenesis of TEMPI syndrome is still not clear, but it has been hypothesized that the monoclonal protein leads to a paraneoplastic syndrome and increased erythropoietin production, similar to the mechanism seen in solid tumors [11].
Sohani et al., "Bone marrow findings of the newly described TEMPI syndrome: When erythrocytosis and plasma cell dyscrasia coexist," Modern Pathology, vol.